Publications

Congenital lung malformations: a nationwide survey on management aspects by the Italian Society of Pediatric Surgery  (2024)

Authors:
Pio, Luca; Gentilino, Valerio; Macchini, Francesco; Scarpa, Alberto Attilio; Lo Piccolo, Roberto; Conforti, Andrea; Ratta, Alberto; Guanà, Riccardo; Molinaro, Francesco; Costanzo, Sara; Riccipetitoni, Giovanna; Lisi, Gabriele; Midrio, Paola; Tocchioni, Francesca; Cobellis, Giovannii; Volpe, Andrea; Zolpi, Elisa; Morandi, Anna; Ciardini, Enrico; Vella, Claudio; Grella, Maria Giovanna; Sergio, Maria; Guida, Edoardo; Nanni, Lorenzo; Ceccanti, Silvia; Di Benedetto, Vincenzo; Cheli, Maurizio; Garzi, Alfredo; Nobili, Maria; Gabriele, Valeria; Boroni, Giovanni; Incerti, Filippo; Zampieri, Nicola; Cacciaguerra, Sebastiano; Ceccarelli, Pier Luca; Escolino, Maria; Briganti, Vito; Gori, Davide; Esposito, Ciro; Gamba, Piergiorgio; Gennari, Fabrizio; Inserra, Alessandro; Dall'Igna, Patrizia; Romeo, Carmelo; Bagolan, Pietro; Bleve, Cosimo; Chiarenza, Fabio; Morini, Francesco; Pelizzo, Gloria; Torre, Michele
Title:
Congenital lung malformations: a nationwide survey on management aspects by the Italian Society of Pediatric Surgery
Year:
2024
Type of item:
Articolo in Rivista
Tipologia ANVUR:
Articolo su rivista
Language:
Inglese
Referee:
No
Name of journal:
PEDIATR. SURG. INT.
ISSN of journal:
0179-0358
N° Volume:
40
Number or Folder:
1
Page numbers:
123-127
Keyword:
CLM, CPAM, Congenital lung malformations, MIS, Pediatric thoracic surgery, Thoracoscopic surgery
Short description of contents:
IntroductionOver the years, congenital lung malformations (CLM) management remains a controversial topic in pediatric thoracic surgery. The Italian Society of Pediatric Surgery performed a national survey to study the current management variability among centers, trying to define national guidelines and a standardized approach of children with congenital lung malformations.MethodsFollowing a National Society approval, an electronic survey including 35 items on post-natal management was designed, focusing on surgical, anesthesiology, radiology and pneumology aspects. The survey was conducted contacting all pediatric surgical units performing thoracic surgery.Results39 pediatric surgery units (97.5%) participated in the study. 13 centers (33.3%) were classified as high-volume (Group A), while 26 centers (66.7%) were low volume (Group B). Variances in diagnostic imaging protocols were observed, with Group A performing fewer CT scans compared to Group B (p = 0.012). Surgical indications favored operative approaches for asymptomatic CLM and pulmonary sequestrations in both groups, while a wait-and-see approach was common for congenital lobar emphysema. Surgical timing for asymptomatic CLM differed significantly, with most high-volume centers operating on patients younger than 12 months (p = 0.02). Thoracoscopy was the preferred approach for asymptomatic CLM in most of centers, while postoperative long-term follow-up was not performed in most of the centers.ConclusionThoracoscopic approach seems uniform in asymptomatic CLM patients and variable in symptomatic children. Lack of uniformity in surgical timing and preoperative imaging assessment has been identified as key areas to establish a common national pattern of care for CLM.
Product ID:
140160
Handle IRIS:
11562/1128787
Last Modified:
October 19, 2024
Bibliographic citation:
Pio, Luca; Gentilino, Valerio; Macchini, Francesco; Scarpa, Alberto Attilio; Lo Piccolo, Roberto; Conforti, Andrea; Ratta, Alberto; Guanà, Riccardo; Molinaro, Francesco; Costanzo, Sara; Riccipetitoni, Giovanna; Lisi, Gabriele; Midrio, Paola; Tocchioni, Francesca; Cobellis, Giovannii; Volpe, Andrea; Zolpi, Elisa; Morandi, Anna; Ciardini, Enrico; Vella, Claudio; Grella, Maria Giovanna; Sergio, Maria; Guida, Edoardo; Nanni, Lorenzo; Ceccanti, Silvia; Di Benedetto, Vincenzo; Cheli, Maurizio; Garzi, Alfredo; Nobili, Maria; Gabriele, Valeria; Boroni, Giovanni; Incerti, Filippo; Zampieri, Nicola; Cacciaguerra, Sebastiano; Ceccarelli, Pier Luca; Escolino, Maria; Briganti, Vito; Gori, Davide; Esposito, Ciro; Gamba, Piergiorgio; Gennari, Fabrizio; Inserra, Alessandro; Dall'Igna, Patrizia; Romeo, Carmelo; Bagolan, Pietro; Bleve, Cosimo; Chiarenza, Fabio; Morini, Francesco; Pelizzo, Gloria; Torre, Michele, Congenital lung malformations: a nationwide survey on management aspects by the Italian Society of Pediatric Surgery «PEDIATR. SURG. INT.» , vol. 40 , n. 12024pp. 123-127

Consulta la scheda completa presente nel repository istituzionale della Ricerca di Ateneo IRIS

<<back
Share